Abernethy Malformation in Children with Focal Liver Lesions
D. E. Arutyunyants,
V. V. Khovrin,
T. N. Galyan,
A. S. Kulichkin,
A. V. Filin,
E. Yu. Kryzhanovskaya https://doi.org/10.20862/0042-4676-2021-102-3-166-171
Abstract
Abernethy malformation is a congenital disease characterized by complete or partial underdevelopment of the portal vein, leading to the occurrence of congenital extrahepatic portosystemic shunts. The anomaly with the absence of the portal vein is detected in 80% of cases in childhood. Patients with this pathology are very frequently examined when detecting space-occupying liver lesions and assuming the presence of a vascular abnormality. The paper describes clinical cases of benign focal liver lesions and Abernethy malformation in children.
About the Authors
D. E. Arutyunyants
Petrovskiy National Research Centre of Surgery
Russian Federation
Russian Federation
Dana E. Arutyunyants, Postgraduate
Abrikosovskiy pereulok, 2, Moscow, 119991
V. V. Khovrin
Petrovskiy National Research Centre of Surgery
Russian Federation
Russian Federation
Valeriy V. Khovrin, Dr. Med. Sc., Chief Researcher
Abrikosovskiy pereulok, 2, Moscow, 119991
T. N. Galyan
Petrovskiy National Research Centre of Surgery
Russian Federation
Russian Federation
Tatyana N. Galyan, Cand. Med. Sc., Head of Department of Radiodiagnostics and Computed Tomography
Abrikosovskiy pereulok, 2, Moscow, 119991
A. S. Kulichkin
Petrovskiy National Research Centre of Surgery
Russian Federation
Russian Federation
Aleksey S. Kulichkin, Radiologist
Abrikosovskiy pereulok, 2, Moscow, 119991
A. V. Filin
Petrovskiy National Research Centre of Surgery
Russian Federation
Russian Federation
Andrey V. Filin, Dr. Med. Sc., Head of Liver Transplant Department
Abrikosovskiy pereulok, 2, Moscow, 119991
E. Yu. Kryzhanovskaya
Petrovskiy National Research Centre of Surgery
Russian Federation
Russian Federation
Evgeniya Yu. Kryzhanovskaya, Cand. Med. Sc., Senior Researcher, Ultrasound Diagnostician
Abrikosovskiy pereulok, 2, Moscow, 119991
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Review
For citations:
Arutyunyants D.E., Khovrin V.V., Galyan T.N., Kulichkin A.S., Filin A.V., Kryzhanovskaya E.Yu. Abernethy Malformation in Children with Focal Liver Lesions. Journal of radiology and nuclear medicine. 2021;102(3):166-171. (In Russ.) https://doi.org/10.20862/0042-4676-2021-102-3-166-171
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