rentradВестник рентгенологии и радиологииJournal of radiology and nuclear medicine0042-46762619-0478Limited Liability Company "LUCHEVAYA DIAGNOSTIKA", Russian Association of Radiologists10.20862/0042-4676-2021-102-3-166-171rentrad-647Research ArticleКЛИНИЧЕСКИЕ СЛУЧАИCASE REPORTSМальформации Абернети у детей с очаговыми образованиями печениAbernethy Malformation in Children with Focal Liver Lesionshttps://orcid.org/0000-0002-7596-4029АрутюнянцД. Э.ArutyunyantsD. E.

Арутюнянц Дана Эдуардовна, аспирант

Абрикосовский пер., 2, Москва, 119991

Dana E. Arutyunyants, Postgraduate

Abrikosovskiy pereulok, 2, Moscow, 119991

dana.aryt@yandex.ruhttps://orcid.org/0000-0002-6720-4126ХовринВ. В.KhovrinV. V.

Ховрин Валерий Владиславович, доктор медицинских наук, главный научный сотрудник

Абрикосовский пер., 2, Москва, 119991

Valeriy V. Khovrin, Dr. Med. Sc., Chief Researcher

Abrikosovskiy pereulok, 2, Moscow, 119991

https://orcid.org/0000-0003-4751-5119ГалянТ. Н.GalyanT. N.

Галян Татьяна Николаевна, кандидат медицинских наук, заведующая отделением рентгенодиагностики и компьютерной томографии

Абрикосовский пер., 2, Москва, 119991

Tatyana N. Galyan, Cand. Med. Sc., Head of Department of Radiodiagnostics and Computed Tomography

Abrikosovskiy pereulok, 2, Moscow, 119991

https://orcid.org/0000-0003-1256-560XКуличкинА. С.KulichkinA. S.

Куличкин Алексей Сергеевич, врач-рентгенолог

Абрикосовский пер., 2, Москва, 119991

Aleksey S. Kulichkin, Radiologist

Abrikosovskiy pereulok, 2, Moscow, 119991

https://orcid.org/0000-0003-4205-5627ФилинА. В.FilinA. V.

Филин Андрей Валерьевич, доктор медицинских наук, заведующий отделением пересадки печени

Абрикосовский пер., 2, Москва, 119991

Andrey V. Filin, Dr. Med. Sc., Head of Liver Transplant Department

Abrikosovskiy pereulok, 2, Moscow, 119991

https://orcid.org/0000-0001-9862-8266КрыжановскаяЕ. Ю.KryzhanovskayaE. Yu.

Крыжановская Евгения Юрьевна, кандидат медицинских наук, старший научный сотрудник, врач ультразвуковой диагностики

Абрикосовский пер., 2, Москва, 119991

Evgeniya Yu. Kryzhanovskaya, Cand. Med. Sc., Senior Researcher, Ultrasound Diagnostician

Abrikosovskiy pereulok, 2, Moscow, 119991

ФГБНУ «Российский научный центр хирургии им. акад. Б.В. Петровского»РоссияPetrovskiy National Research Centre of SurgeryRussian Federation2021220720211023166171Copyright © Арутюнянц Д.Э., Ховрин В.В., Галян Т.Н., Куличкин А.С., Филин А.В., Крыжановская Е.Ю., 20212021Арутюнянц Д.Э., Ховрин В.В., Галян Т.Н., Куличкин А.С., Филин А.В., Крыжановская Е.Ю.Arutyunyants D.E., Khovrin V.V., Galyan T.N., Kulichkin A.S., Filin A.V., Kryzhanovskaya E.Y.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.russianradiology.ru/jour/article/view/647

Мальформация Абернети – врожденное заболевание, характеризующееся полным или частичным недоразвитием воротной вены и приводящее к возникновению врожденных внепеченочных портосистемных шунтов. Аномалия с отсутствием воротной вены в 80% случаев обнаруживается в детском возрасте. Очень часто пациенты с данной патологией обследуются при выявлении объемных образований печени с предположением о наличии сосудистой аномалии. В статье представлены клинические наблюдения детей с доброкачественными очаговыми образованиями печени и наличием мальформации Абернети.

Abernethy malformation is a congenital disease characterized by complete or partial underdevelopment of the portal vein, leading to the occurrence of congenital extrahepatic portosystemic shunts. The anomaly with the absence of the portal vein is detected in 80% of cases in childhood. Patients with this pathology are very frequently examined when detecting space-occupying liver lesions and assuming the presence of a vascular abnormality. The paper describes clinical cases of benign focal liver lesions and Abernethy malformation in children.

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The authors declare that there are no conflicts of interest present.