DIAGNOSIS AND TREATMENT POLICY FOR SEVERE CONGENITAL CYSTIC ADENOMATOID MALFORMATION OF THE LUNG IN NEWBORN INFANTS

Objective. To present the diagnosis of and treatment policy for severe cystic adenomatoid malformation (CAM) of the lung in newborn infants, allowing one to rule out a fatal outcome and to ensure good quality of life in the future. Material and methods. The authors describe their own 12 clinical cases in newborn infants with the histologically verified diagnosis of type 1 CAM with a pronounced mass effect, as well as pregnancy management tactics, the time and algorithm of postnatal radiation examination, a treatment method and give long-term results. Results. The traced long-term results are predominantly good (77.8%); there are no poor outcomes or mortality in this patient group. Conclusion. The prognosis for life in severe forms of CAM with a high risk of antepartum fetal demise can be favorable if there is a correct pregnancy management tactics, early examination, and surgical treatment. Computed tomography and computed tomographic angiography are main postnatal diagnostic techniques that determine the further tactics of a neonatal surgeon. Emergency surgery is indicated after the diagnosis of type 1 CAM with a pronounced mass effect is confirmed.

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